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Gerstmann Syndrome

National Organization for Rare Disorders, Inc.

Important
It is possible that the main title of the report Gerstmann Syndrome is not the name you expected. Please check the synonyms listing to find the alternate name(s) and disorder subdivision(s) covered by this report.

Synonyms

  • Developmental Gerstmann Syndrome
  • Gerstmann Tetrad
  • GS

Disorder Subdivisions

  • None

General Discussion

Gerstmann syndrome is a rare neurological disorder that can occur as the result of a brain injury or as a developmental disorder. The syndrome is characterized by the loss or absence of four cognitive abilities- the loss of the ability to express thoughts in writing (agraphia, dysgraphia), to perform simple arithmetic problems (acalculia), to recognize or indicate one's own or another's fingers (finger agnosia), and to distinguish between the right and left sides of one's body. Additional cognitive defects may occur in some cases.

The disorder has not been found to run in families. In extremely rare cases, children who are bright and functioning intellectually at a high level may be affected by the disorder as well as those who suffer brain damage.

Gerstmann syndrome is different from Gerstmann-Sträussler-Scheinker syndrome, a rare genetic degenerative brain disorder.

Resources

National Center for Learning Disabilities
381 Park Avenue South
1420 Suite
New York, NY 10016
Tel: (212)545-7510
Fax: (212)545-9665
Tel: (888)575-7373
Email: ncld@ncld.org
Internet: http://www.ncld.org/

Learning Disabilities Association of America
4156 Library Road
Pittsburgh, PA 15234-1349
Tel: (412)341-1515
Fax: (412)344-0224
Tel: (888)300-6710
Email: info@ldaamerica.org
Internet: http://www.ldanatl.org

American Speech-Language-Hearing Association
2200 Research Boulevard
Rockville, MD 20850-3289
United States
Tel: (301)296-5700
Fax: (301)296-8580
Tel: (800)638-8255
Email: actioncenter@asha.org
Internet: http://www.asha.org

NIH/National Institute of Neurological Disorders and Stroke
P.O. Box 5801
Bethesda, MD 20824
Tel: (301)496-5751
Fax: (301)402-2186
Tel: (800)352-9424
TDD: (301)468-5981
Internet: http://www.ninds.nih.gov/

Genetic and Rare Diseases (GARD) Information Center
PO Box 8126
Gaithersburg, MD 20898-8126
Tel: (301)251-4925
Fax: (301)251-4911
Tel: (888)205-2311
TDD: (888)205-3223
Internet: http://rarediseases.info.nih.gov/GARD/

For a Complete Report

This is an abstract of a report from the National Organization for Rare Disorders (NORD). A copy of the complete report can be downloaded free from the NORD website for registered users. The complete report contains additional information including symptoms, causes, affected population, related disorders, standard and investigational therapies (if available), and references from medical literature. For a full-text version of this topic, go to www.rarediseases.org and click on Rare Disease Database under "Rare Disease Information".

The information provided in this report is not intended for diagnostic purposes. It is provided for informational purposes only. NORD recommends that affected individuals seek the advice or counsel of their own personal physicians.

It is possible that the title of this topic is not the name you selected. Please check the Synonyms listing to find the alternate name(s) and Disorder Subdivision(s) covered by this report

This disease entry is based upon medical information available through the date at the end of the topic. Since NORD's resources are limited, it is not possible to keep every entry in the Rare Disease Database completely current and accurate. Please check with the agencies listed in the Resources section for the most current information about this disorder.

For additional information and assistance about rare disorders, please contact the National Organization for Rare Disorders at P.O. Box 1968, Danbury, CT 06813-1968; phone (203) 744-0100; web site www.rarediseases.org or email orphan@rarediseases.org

Last Updated:  3/27/2008
Copyright  1993, 1997, 2002, 2008 National Organization for Rare Disorders, Inc.

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